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Clinical Approach to MCAS Diagnosis and Cutaneous Mastocytosis

Table 2. Differential diagnosis of MCAS

Neoplastic

 Neuroendocrine tumors (gastrinoma,  VIPoma, medullary thyroid carcinoma, pheocromocytoma, carcinoid syndrome)

Inflammatory

 Inflammatory bowel disease 

 Hyper-eosinophilic syndromes 

 Vasculitis

Vascular

 Hereditary angioedema (HAE)  

 Acquired angioedema  

 Renal or hepatic insufficiency

Endocrine

Adrenal disease Hypothyroidism

InfectionsParasites 

Viral-/bacterial-induced hives

Toxic

 Scromboid poisoning 

 Aspirin-exacerbated respiratory disease


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